Asian Journal of Cardiology Research

Mitigating the Double-Edged Sword: Percutaneous Intervention for Lutembacher’s Syndrome

Kalyan Munde

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

Mohan Paliwal *

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

Anant Munde

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

Samkit Mutha

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

Hariom Kolapkar

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

Anagh T S

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

Jayakrishna Niari

Department of Cardiology, Grant Government Medical College and Sir J.J. Group of Hospitals, Mumbai, Maharashtra, India.

*Author to whom correspondence should be addressed.

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Abstract

Lutembacher’s syndrome (LS) is a very rare condition and is characterized by a congenital ostium secundum type atrial septal defect (OS-ASD) and an acquired mitral stenosis (MS) which is commonly rheumatic in origin, most common in females. Here we report a case of a 35-year-old male with Lutembacher's syndrome who underwent balloon mitral valvuloplasty (BMV) and device closure of the atrial septal defect (ASD). Previously the treatment preferred for patients with LS was surgical but in today’s era, transcatheter intervention should be preferred in suitable patients. Because of the large ASD, BMV necessitated technical modification of taking the Accura balloon over the wire (OTW) into the left ventricle (LV), and also larger ASD device had to be used to prevent device embolization.

Keywords: Lutembacher's syndrome, atrial septal defect, mitral stenosis, BMV, Balloon manipulation, device closure, percutaneous intervention

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